946-1 Progressive External Ophthalmoplegia

Identifier: 946-1 Title: Progressive External Ophthalmoplegia Subject: Bilateral Ptosis; Facial Weakness; Complete External Ophthalmoplegia; Bilateral Progressive External Ophthalmoplegia (PEO); Mitochondrial Myopathy; PEO plus Atypical Retinitis Pigmentosa, Heart Block, Deafness, Proximal Myopathy and Cerebellar Degeneration with Ataxia; Kearns-Sayre Syndrome; Description: In 1995 I published this case alongside eleven personal cases, three with the Kearns-Sayer Syndrome (KSS) and five with Progressive External Opthalmoplegia (PEO). Am J of Neuroradiol:16 (5);1167-1173. This patient with KSS is still alive in 2009. In 1968, at the age of 15 he presented with a history of childhood strabismus treated surgically and the insidious onset of slowly progressive asymmetrical ptosis right eye greater than left eye. This video is part of the Wray Collection in NOVEL, the Neuro-Ophthalmology Virtual Education Library. Please cite the source when using this video. NOVEL.utah.edu Copyright 2015. For further information regarding the rights to this collection, please visit http://library.med.utah.edu/NOVEL/about/copyright